Chronic kidney disease with malignant peripheral nerve sheath tumor of the ureter: a case report

TL;DR

A rare case of a kidney disease patient with a malignant tumor in the ureter is reported, with successful surgical treatment and no recurrence.

Contribution

This case report highlights an extremely rare occurrence of MPNST in the ureter combined with stage 5 chronic kidney disease.

Findings

A 63-year-old patient had a malignant peripheral nerve sheath tumor in the right ureter.

The patient underwent laparoscopic radical resection and showed no tumor recurrence during follow-up.

Due to stage 5 chronic kidney disease, chemotherapy and radiotherapy were not administered.

Abstract

Malignant peripheral nerve sheath tumors (MPNSTs) are a complex group of malignant tumors originating from nerve cells or benign peripheral nerve sheath tumors and are commonly found in major plexus/nerve root sites such as the limbs, head, and neck. Malignant peripheral nerve sheath tumors originating in the ureter are extremely rare. Herein, we report the case of a 63-year-old patient with a malignant peripheral nerve sheath tumor of the right ureter who underwent laparoscopic radical resection of the right kidney and ureter. The patient also had stage 5 chronic kidney disease (CKD). Therefore, chemotherapy and radiotherapy were not considered. No tumor recurrence was observed during the follow-up period.

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