# Chronic kidney disease with malignant peripheral nerve sheath tumor of the ureter: a case report

## TL;DR

A rare case of a kidney disease patient with a malignant tumor in the ureter is reported, with successful surgical treatment and no recurrence.

## Contribution

This case report highlights an extremely rare occurrence of MPNST in the ureter combined with stage 5 chronic kidney disease.

## Key findings

- A 63-year-old patient had a malignant peripheral nerve sheath tumor in the right ureter.
- The patient underwent laparoscopic radical resection and showed no tumor recurrence during follow-up.
- Due to stage 5 chronic kidney disease, chemotherapy and radiotherapy were not administered.

## Abstract

Malignant peripheral nerve sheath tumors (MPNSTs) are a complex group of malignant tumors originating from nerve cells or benign peripheral nerve sheath tumors and are commonly found in major plexus/nerve root sites such as the limbs, head, and neck. Malignant peripheral nerve sheath tumors originating in the ureter are extremely rare. Herein, we report the case of a 63-year-old patient with a malignant peripheral nerve sheath tumor of the right ureter who underwent laparoscopic radical resection of the right kidney and ureter. The patient also had stage 5 chronic kidney disease (CKD). Therefore, chemotherapy and radiotherapy were not considered. No tumor recurrence was observed during the follow-up period.