A Giant Primary Angiosarcoma Invading the Right Heart in a Young Male: An Emergency Surgery

TL;DR

A 25-year-old man with a rare giant heart tumor underwent emergency surgery, which confirmed it was a primary cardiac angiosarcoma.

Contribution

This case report presents a rare instance of a giant primary cardiac angiosarcoma managed through emergency surgery.

Findings

Emergency surgery was performed to remove a giant angiosarcoma invading the right heart.

Histopathology confirmed the tumor as a primary cardiac angiosarcoma.

The patient experienced severe postoperative complications including right ventricular dysfunction and multiorgan failure.

Abstract

Primary cardiac angiosarcoma is very rare. In this report, we describe an interesting case of a 25-year-old male with a giant primary angiosarcoma invading the right heart. He was urgently admitted to the hospital for respiratory distress. Once the diagnosis was suspected by chest x-ray, echocardiography, and CT scan, and given the patient's hemodynamic and respiratory instability, an emergency open-heart surgery was necessary to prevent complications. Through a right atriotomy and a pulmonary infundibulotomy, the tumor was resected. Invaded by the tumoral process, the tricuspid valve was replaced with a biological prosthesis. The postoperative course was marked by severe right ventricular dysfunction with multiorgan failure. Histopathologic examination of the surgical specimen confirmed a primary cardiac angiosarcoma.

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