# A Giant Primary Angiosarcoma Invading the Right Heart in a Young Male: An Emergency Surgery

## TL;DR

A 25-year-old man with a rare giant heart tumor underwent emergency surgery, which confirmed it was a primary cardiac angiosarcoma.

## Contribution

This case report presents a rare instance of a giant primary cardiac angiosarcoma managed through emergency surgery.

## Key findings

- Emergency surgery was performed to remove a giant angiosarcoma invading the right heart.
- Histopathology confirmed the tumor as a primary cardiac angiosarcoma.
- The patient experienced severe postoperative complications including right ventricular dysfunction and multiorgan failure.

## Abstract

Primary cardiac angiosarcoma is very rare. In this report, we describe an interesting case of a 25-year-old male with a giant primary angiosarcoma invading the right heart. He was urgently admitted to the hospital for respiratory distress. Once the diagnosis was suspected by chest x-ray, echocardiography, and CT scan, and given the patient's hemodynamic and respiratory instability, an emergency open-heart surgery was necessary to prevent complications. Through a right atriotomy and a pulmonary infundibulotomy, the tumor was resected. Invaded by the tumoral process, the tricuspid valve was replaced with a biological prosthesis. The postoperative course was marked by severe right ventricular dysfunction with multiorgan failure. Histopathologic examination of the surgical specimen confirmed a primary cardiac angiosarcoma.