# Systematized Linear Porokeratosis With Palmoplantar and Nail Involvement: A Rare Presentation

## TL;DR

This paper reports a rare case of linear porokeratosis in a 48-year-old man with palm, sole, and nail involvement, highlighting the need for long-term monitoring due to cancer risk.

## Contribution

The case presents a rare combination of palmoplantar and nail involvement in systematized linear porokeratosis.

## Key findings

- The patient had childhood-onset linear porokeratosis with palmoplantar and nail involvement.
- Linear porokeratosis is associated with a high risk of malignancy and requires long-term surveillance.
- This case adds to the limited literature on rare clinical presentations of porokeratosis.

## Abstract

Porokeratosis encompasses a group of genetically and clinically heterogenous dermatoses characterized by abnormal epidermal keratinization, with the cornoid lamella being the hallmark histological feature. Linear porokeratosis, a rare variant of porokeratosis, typically manifests early in life, with lesions that follow the lines of Blaschko and carry the highest risk of malignancy transformation. Here, we present a case of systematized linear porokeratosis in a 48-year-old male with childhood onset, notable for the rare co-existence of palmoplantar and nail involvement. This report emphasizes the importance of long-term surveillance in patients with linear porokeratosis due to its malignant potential.