# Rare Case of Multifocal Spinal Hemangioblastomas With Holocord Syringo-Hydromyelia in an Adolescent Male

**Authors:** Rishi Meswani, Prashant Onkar, Suresh Phatak, Kajal Mitra, Mayank Rangari

PMC · DOI: 10.7759/cureus.102651 · Cureus · 2026-01-30

## TL;DR

This paper describes a rare case of multiple spinal tumors and fluid-filled channels in a teenager without a known genetic condition.

## Contribution

The novelty lies in reporting multifocal spinal hemangioblastomas with holocord syringo-hydromyelia in an adolescent without von Hippel-Lindau syndrome.

## Key findings

- Multifocal spinal hemangioblastomas were identified in an adolescent male.
- The case was associated with extensive holocord syringo-hydromyelia.
- No evidence of von Hippel-Lindau syndrome was found in the patient.

## Abstract

Hemangioblastomas are benign, highly vascular tumors of the central nervous system. Although they most commonly arise in the cerebellum, they may also involve the brainstem and spinal cord. The presence of multiple spinal hemangioblastomas is frequently associated with von Hippel-Lindau (VHL) syndrome; however, sporadic cases without an underlying genetic syndrome can occur. Characteristic imaging features include avid post-contrast enhancement, associated syrinx formation, and intratumoral or peritumoral flow voids. Spinal hemangioblastomas account for a small proportion of intramedullary spinal tumors and are rarely reported in adolescents. We present a rare case of multifocal spinal hemangioblastomas with extensive holocord syringo-hydromyelia in an adolescent male patient without any evidence of VHL syndrome.

## Full-text entities

- **Diseases:** thoracic lesion (MESH:D013896), -sided weakness (MESH:D018908), tumor (MESH:D009369), localized pain (MESH:D010146), inflammatory (MESH:D007249), ependymoma (MESH:D004806), genetic disorder (MESH:D030342), fever (MESH:D005334), hemorrhage (MESH:D006470), intramedullary lesion (MESH:D013120), infective (MESH:D007239), VHL syndrome (MESH:D006623), neurological impairment (MESH:D009422), astrocytoma (MESH:D001254), Hemangioblastomas (MESH:D018325), sporadic multifocal disease (MESH:D020821)
- **Chemicals:** gadolinium (MESH:D005682)
- **Species:** Homo sapiens (human, species) [taxon 9606]

## Full text

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## Figures

3 figures with captions in the complete paper: https://tomesphere.com/paper/PMC12951011/full.md

## References

9 references — full list in the complete paper: https://tomesphere.com/paper/PMC12951011/full.md

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Source: https://tomesphere.com/paper/PMC12951011