Transcatheter Correction of Bilateral Partial Anomalous Pulmonary Venous Return with Intrapulmonary Dual Drainage: A Rare Entity

TL;DR

A rare heart condition in a 6-year-old boy was successfully treated using a minimally invasive catheter procedure.

Contribution

This case report presents a novel transcatheter approach for treating bilateral partial anomalous pulmonary venous return with intrapulmonary dual drainage.

Findings

Balloon occlusion testing confirmed no venous congestion in the upper lung fields.

Transcatheter occlusion using vascular plugs was performed safely and successfully.

The procedure preserved intrapulmonary collateral venous connections.

Abstract

Partial anomalous pulmonary venous return (PAPVR) with dual drainage is a very rare congenital heart anomaly. We report the case of a 6-year-old boy with PAPVR in whom both upper pulmonary veins (PVs) drain anomalously into the systemic venous circulation, while maintaining preserved intrapulmonary collateral venous connections with the remaining pulmonary veins draining into the left atrium. Careful balloon occlusion testing of the anomalous PVs was performed, simultaneously with measurements of pulmonary pressures and control angiography, proving the absence of venous congestion in the upper lung fields during the pulmonary venous phase. Transcatheter occlusion using vascular plugs was safely and successfully performed.

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