# A Case of Ganglionopathy Presenting with Hyperkinetic Movements

## TL;DR

This paper describes a rare neurological condition called sensory ganglionopathy linked to Sjogren’s disease, presenting with unusual movement symptoms.

## Contribution

The paper highlights a rare and underrecognized manifestation of Sjogren’s disease through a detailed case report.

## Key findings

- A 73-year-old man exhibited sensory ataxia and pseudoathetosis due to Sjogren’s-related ganglionopathy.
- MRI and EMG findings indicated polyneuropathy, with elevated CSF protein and positive Sjogren’s antibodies.
- The case emphasizes the importance of early recognition of this rare condition.

## Abstract

Sensory ganglionopathy is a rare, often underrecognized neurological manifestation of Sjogren’s disease, presenting with non–length-dependent sensory symptoms that may mimic other neuropathies.

We report a case of Sjogren’s-related sensory ganglionopathy presenting as severe sensory ataxia and pseudoathetosis. A 73-year-old man developed involuntary movements, sensory loss, and gait ataxia. Exam showed absent proprioception, areflexia, and worsening ataxia with eye closure. MRI revealed degenerative spine disease; EMG showed demyelinating and axonal polyneuropathy. CSF protein was elevated and Sjogren’s antibodies were positive.

Progressive sensory ataxia despite immunotherapy confirmed Sjogren’s-associated sensory ganglionopathy emphasizing the importance of early recognition.