# Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome: A Case Report

**Authors:** Yin Ru Tan, Ravichandran Nadarajah, Hak Koon Tan

PMC · DOI: 10.7759/cureus.101002 · Cureus · 2026-01-07

## TL;DR

This paper reports a successful surgical treatment of a rare congenital condition called OHVIRA syndrome, which causes cyclical pain in affected individuals.

## Contribution

The novelty lies in presenting a case of OHVIRA syndrome with successful surgical management and highlighting the importance of accurate diagnosis.

## Key findings

- OHVIRA syndrome was diagnosed and managed successfully through surgery.
- Accurate diagnosis is crucial for symptom relief and prevention of complications.
- The case highlights the typical presentation of cyclical pain after menarche.

## Abstract

Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare congenital genitourinary tract anomaly characterized by the triad of uterine didelphys, unilateral obstructed hemivagina, and ipsilateral renal agenesis. Patients typically present with symptoms of cyclical pain after menarche. Cases are usually complex and may pose difficulties in diagnosis and management. Accurate diagnosis and prompt treatment are essential to relieve patient symptoms and prevent complications. We present a case of OHVIRA syndrome that was successfully managed surgically.

## Linked entities

- **Diseases:** OHVIRA syndrome (MONDO:0008636)

## Full-text entities

- **Diseases:** obstructed hemivagina (MESH:D000402), pain (MESH:D010146), renal agenesis (MESH:C536482), uterine didelphys (MESH:D000093642), congenital genitourinary tract anomaly (MESH:C564424), OHVIRA syndrome (MESH:D012078)
- **Species:** Homo sapiens (human, species) [taxon 9606]

## Full text

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## Figures

8 figures with captions in the complete paper: https://tomesphere.com/paper/PMC12880842/full.md

## References

13 references — full list in the complete paper: https://tomesphere.com/paper/PMC12880842/full.md

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Source: https://tomesphere.com/paper/PMC12880842