# From Fetal Diagnosis to Staged Percutaneous Palliation: A Case of Double Right-Valve Dysplasia

## TL;DR

This paper presents a case where early diagnosis and staged treatment of rare heart valve issues in a fetus led to successful long-term outcomes.

## Contribution

The paper demonstrates a successful staged percutaneous palliation approach for double right-valve dysplasia, promoting right ventricle growth.

## Key findings

- Prenatal diagnosis enabled timely planning for biventricular repair.
- Staged interventions improved clinical outcomes and right ventricle development.
- Early palliation can avoid univentricular repair and improve long-term prognosis.

## Abstract

Tricuspid valve dysplasia (TVD) and pulmonary valve dysplasia (PVD) are rare congenital anomalies that challenge prenatal counseling and postnatal care. When feasible, biventricular repair is the highest priority choice.

We report a prenatal diagnosis of non-Ebstein TVD with severe regurgitation, hypoplastic right ventricle (RV), and PVD with an intact ventricular septum. Prenatal counseling illustrated the potential ventricular repair plan. During the postnatal period, pulmonary valvuloplasty was performed, followed by stenting of the ductus arteriosus. The patient demonstrated clinical improvement, a progressive increase in RV size, and satisfactory pulmonary flow over time.

This case highlights the significance of early intervention in facilitating RV growth and maximizing biventricular circulation. The literature describes staged catheter-based approaches as therapies that can avoid univentricular palliation.

Prenatal diagnosis of TVD with PVD enables timely planning and early biventricular repair, promising better long-term outcomes. A staged, personalized approach can promote RV growth.