# Hypovolemic shock due to massive subcutaneous hemorrhage in a patient with musculocontractural Ehlers-Danlos syndrome (mcEDS)

## TL;DR

A young man with a rare connective tissue disorder experienced severe bleeding after minor trauma, highlighting the need for early recognition and specialized care.

## Contribution

This case report emphasizes the risk of life-threatening bleeding in mcEDS and advocates for multidisciplinary management.

## Key findings

- A patient with mcEDS developed a massive subcutaneous hematoma after minor trauma.
- Surgical evacuation was required to manage the life-threatening hemorrhage.
- Early recognition and coordinated care are critical in managing mcEDS complications.

## Abstract

Musculocontractural Ehlers-Danlos syndrome (mcEDS) is a rare autosomal recessive connective tissue disorder characterized by fragility of skin, vasculature and musculoskeletal structures. We report a case of a young male with CHST14(Carbohydrate sulfotransferase 14)-related mcEDS who developed a massive subcutaneous hematoma following minor trauma, necessitating surgical evacuation. This case highlights the potential for life-threatening bleeding complications in mcEDS and underscores the importance of early recognition and multidisciplinary management.