# A rare case of isolated unilateral pulmonary vein atresia presenting as interstitial lung disease in a young adult

## TL;DR

A 21-year-old adult was diagnosed with a rare heart condition causing lung disease, typically seen in children.

## Contribution

Presentation of a rare adult case of isolated unilateral pulmonary vein atresia with interstitial lung disease.

## Key findings

- Unilateral pulmonary vein atresia was diagnosed in a 21-year-old adult.
- The condition presented as unilateral interstitial lung disease.
- This case highlights the rare occurrence of the condition beyond childhood.

## Abstract

Unilateral pulmonary vein atresia is an unusual congenital cardiovascular abnormality. It occurs due to failure of incorporation of pulmonary veins into the left atrium. It is usually diagnosed in childhood and diagnosis after adulthood is very rare. Herein we present a case of 21-year-old young adult with isolated unilateral pulmonary vein atresia who presented with unilateral interstitial lung disease.