# A Case of Type 1 Congenital Pulmonary Airway Malformation (CPAM) in an Eight-Year-Old Girl Without a History of Recurrent Pneumonia or Respiratory Failure, Presenting With a Pulmonary Abscess

## TL;DR

An eight-year-old girl with no prior lung issues was diagnosed with a rare lung condition after developing a pulmonary abscess.

## Contribution

This case highlights the atypical presentation of Type 1 CPAM without prior respiratory symptoms in a school-aged child.

## Key findings

- Type 1 CPAM was diagnosed in an eight-year-old girl who presented with a pulmonary abscess, not typical symptoms like pneumonia.
- Surgical resection led to no recurrence, emphasizing its effectiveness even in atypical cases.
- The case underscores the need to consider congenital lung disease when diagnosing pediatric pulmonary abscesses.

## Abstract

Congenital pulmonary airway malformation (CPAM) is a rare developmental anomaly of the lung, most often diagnosed in infancy or early childhood due to recurrent pneumonia or respiratory distress. We report the case of an eight-year-old girl who presented with fever, cough, hemoptysis, and chest pain, and was ultimately found to have pulmonary abscesses in the right upper and middle lobes. She had no prior history of recurrent respiratory infections or neonatal distress. Chest computed tomography revealed multilocular cystic lesions involving two lobes, raising suspicion for CPAM. The patient received prolonged intravenous and oral antibiotic therapy, followed by surgical resection consisting of a right upper lobectomy and wedge resection of the middle lobe. Histopathological examination confirmed Type 1 CPAM. She has remained free of recurrence since surgery. This case is notable for the unusually late presentation of Type 1 CPAM in school-aged children without prior symptoms, discovered only after the development of pulmonary abscesses. The absence of recurrent pneumonia or abnormal imaging made differentiation from a primary pulmonary abscess challenging. Given the risks of recurrent infections and malignant transformation, including mucinous adenocarcinoma and pleuropulmonary blastoma, surgical resection remains the preferred treatment, even in atypical or incidentally detected cases. This report underscores the importance of considering congenital cystic lung disease in the differential diagnosis of pediatric pulmonary abscess and highlights the role of thorough evaluation and timely surgical management in achieving favorable outcomes.