# Skeletonized Handmade Valved Conduit: A Novel Approach for Transannular Repair in Absent Pulmonary Valve Syndrome

## TL;DR

A new surgical technique using a handmade valved conduit successfully repaired a rare heart defect in a young patient with limited anatomical space.

## Contribution

A novel half-skeletonized handmade valved conduit is introduced for transannular repair in absent pulmonary valve syndrome.

## Key findings

- The conduit provided effective right ventricular outflow tract reconstruction with minimal airway obstruction.
- Postoperative imaging confirmed bronchial decompression and sustained valve function at 1 year.
- The technique addresses limitations of homografts and may be applicable to other congenital heart defects.

## Abstract

Absent pulmonary valve syndrome in neonates and infants presents challenges due to airway compression from dilated pulmonary arteries and limited anatomical space for right ventricular outflow tract (RVOT) reconstruction. This study introduces a half-skeletonized handmade valved conduit for transannular repair in a 6-month-old boy with absent pulmonary valve syndrome, trisomy 21, and laryngomalacia. The conduit, made from expanded polytetrafluoroethylene, provided effective RVOT reconstruction while minimizing airway obstruction. Postoperative imaging confirmed bronchial decompression, and echocardiography showed sustained valve function at 1 year. This technique addresses homograft limitations and may have broader applicability in congenital heart defects requiring RVOT reconstruction.