Desmoid fibromatosis of the cruris: A rare case report

TL;DR

This paper reports a rare case of desmoid fibromatosis in the thigh, a non-cancerous but locally aggressive tumor.

Contribution

The contribution is a detailed clinical case report of desmoid fibromatosis in a rare anatomical location.

Findings

Desmoid fibromatosis is a rare tumor with high local recurrence potential.

The tumor typically affects females aged 15–60 and is commonly found in extremities or abdominal regions.

DF is classified as an intermediate, locally aggressive tumor by the WHO.

Abstract

Desmoid Fibromatosis (DF) is a locally aggressive connective tissue neoplasm that arises within the musculoaponeurotic structures. It is also referred to by various terms, including aggressive fibromatosis, deep fibromatosis, musculoaponeurotic fibromatosis, and desmoid tumor. DF is a rare tumor, with a reported incidence of 2–4 cases per million population, accounting for approximately 0.03% of all neoplasms. It most commonly occurs between the ages of 15 and 60 years and tends to be more prevalent in females. Although DF can develop in various anatomical locations, it is most frequently observed in the extremities, abdominal wall, and intra-abdominal mesentery. Despite lacking metastatic potential, DF has a high propensity for local recurrence. Due to these biological characteristics, DF is currently classified as an “intermediate, locally aggressive” tumor according to the World Health Organization (WHO) classification of soft tissue tumors. This report presents a clinical case of desmoid fibromatosis.

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