# A perivascular epithelioid cell neoplasm of the bladder diagnosed after six years: A case report

## TL;DR

This case report describes a rare bladder tumor diagnosed after a six-year delay, highlighting the challenges in identifying and treating this condition.

## Contribution

The novelty lies in presenting a delayed diagnosis of bladder PEComa and reviewing recent studies to aid in clinical recognition.

## Key findings

- Bladder PEComa is rare and lacks standardized diagnostic protocols.
- Delayed diagnosis occurred due to challenges in recognizing the tumor's features.
- Review of recent studies aims to improve clinician awareness and reduce misdiagnosis.

## Abstract

Perivascular epithelioid cell neoplasm (PEComa) is a rare mesenchymal-derived tumor with specific histological and immunohistochemical manifestations. Given the rarity of bladder PEComa, standardized diagnostic and therapeutic protocols have yet to be established. This article presents a case of bladder PEComa that was ultimately diagnosed after a six-year delay and reviews recent studies to improve clinicians' understanding of this tumor and minimize the risk of misdiagnosis.