# A Rare Clinical Presentation of Congenital Superficial Angiomyxoma: A Case Report

## TL;DR

This case report describes a rare congenital form of superficial angiomyxoma in the vulvar region, observed from birth and growing over two years.

## Contribution

The report presents the third documented case of congenital vulvar superficial angiomyxoma, expanding clinical understanding of its rare presentation.

## Key findings

- Superficial angiomyxoma can present congenitally in the vulvar region.
- The lesion showed gradual growth over two years, appearing as a pedunculated, red, jelly-like mass.

## Abstract

Angiomyxoma is a rare atypical mesenchymal proliferation with two distinct forms, deep and superficial. Superficial Angiomyxoma tends to be benign with limited skin involvement. Rarely, Superficial Angiomyxoma appears in the vulvar region in the form of cystic, vascular, or tumoral lesions. The onset of vulvar superficial angiomyxoma is variable and ranges from early childhood to the post‐menopausal period. To the best of our knowledge, this report presents the third documented case of vulvar superficial angiomyxoma with an onset at birth and a subsequent gradual increase in size over 2 years.

A pedunculated, cauliflower red‐colored, jelly mass in the left vulvar region (A) & (B).