A rare paediatric mandibular desmoid tumour: emphasis on growth-conscious resection and reconstructive strategy

TL;DR

A rare case of a jaw tumor in a teenager is described, emphasizing careful surgical removal and reconstruction to preserve function and appearance.

Contribution

This case report presents a growth-conscious surgical approach for a rare pediatric mandibular tumor.

Findings

A 15-year-old patient had successful hemimandibulectomy with condyle preservation for desmoid-type fibromatosis.

Immediate reconstruction using a titanium plate maintained facial aesthetics and oral function.

No tumor recurrence was observed at the 12-month follow-up.

Abstract

Desmoid-type fibromatosis (DTF) of the mandible is a rare, benign histological tumour that behaves aggressively in paediatric patients. We report the case of a 15-year-old boy with a 1-year history of a painless mandibular mass resulting in facial asymmetry. Imaging revealed a large, well-defined lesion of the right mandibular ramus and angle. Incisional biopsy confirmed DTF. Surgical resection was performed via hemimandibulectomy with preservation of the condyle. Immediate reconstruction was achieved using a titanium plate, preserving both facial aesthetics and oral function. Histopathological analysis confirmed complete excision with tumour-free margins. No recurrence was observed at the 12-month follow-up. This case highlights the importance of a growth-sensitive surgical strategy and multidisciplinary collaboration in managing paediatric mandibular DTF.

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