# A Rare Case of Shone Complex With a Persistent Left Superior Vena Cava and Absent Right Superior Vena Cava

**Authors:** Balaji Aironi, Gaurish Sawant, Palakkumar P Shah, Hitesh Makhija, Rajat Lohiya

PMC · DOI: 10.7759/cureus.85658 · 2025-06-09

## TL;DR

This paper reports a rare case of Shone complex with unusual vascular anomalies, highlighting the need for thorough clinical evaluation.

## Contribution

The novelty lies in describing an incomplete Shone complex with a persistent left and absent right superior vena cava.

## Key findings

- The case involved incomplete Shone complex with multiple left heart obstructions.
- A persistent left superior vena cava and absent right superior vena cava were identified as additional anomalies.
- Comprehensive clinical workup was essential for accurate diagnosis and surgical planning.

## Abstract

Shone complex is a rare and underrecognized congenital heart disease involving four obstructive lesions of the left heart. This report presents a rare case of incomplete Shone complex, along with other associated anomalies, requires an extensive clinical workup for accurate diagnosis and appropriate surgical planning.

## Linked entities

- **Diseases:** Shone complex (MONDO:0020404)

## Full-text entities

- **Diseases:** heart (MESH:D006331), Shone Complex (MESH:D048090), obstructive lesions (MESH:D008173), congenital heart disease (MESH:D006330)

## Figures

2 figures with captions in the complete paper: https://tomesphere.com/paper/PMC12241439/full.md

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Source: https://tomesphere.com/paper/PMC12241439