Emergency 33-Week Cesarean Section With 3.4 cm Type A Aortic Dissection Repair in a Patient With Marfan Syndrome: A Multidisciplinary Approach

TL;DR

A 26-year-old pregnant woman with Marfan syndrome and aortic dissection successfully had emergency surgery to deliver her baby and repair her aorta, showing the importance of teamwork among medical specialists.

Contribution

This case demonstrates a successful multidisciplinary approach to managing a rare and high-risk pregnancy complication involving aortic dissection and Marfan syndrome.

Findings

Concomitant cesarean section and aortic repair was successfully performed at 33 weeks gestation.

Multidisciplinary coordination led to recovery of both mother and infant without major complications.

Early recognition and imaging are critical for managing aortic dissection in high-risk pregnancies.

Abstract

Aortic dissection (AoD) in pregnancy, particularly in women with Marfan syndrome (MFS), carries a high risk for both maternal and fetal mortality. Multidisciplinary management is essential for successful outcomes in these complex cases. We present a 26-year-old G1P0 female patient at 33 weeks gestation with chronic hypertension and MFS who developed mild symptoms of type A AoD. She underwent successful concomitant cesarean section and emergency aortic repair. Through multidisciplinary coordination of obstetrics with cardiothoracic surgery (CTS) and neonatal teams, both mother and infant recovered without major complications. This case highlights the critical need for early recognition, imaging, and multidisciplinary collaboration in pregnant patients with known risk factors of life-threatening conditions, such as AoD. Stricter screening protocols and frequent monitoring may prevent catastrophic outcomes in these high-risk patients.

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