# Role of Computed Tomography Findings in Diagnosing Pulmonary Atresia With Intact Ventricular Septum and Right Ventricle-Dependent Coronary Circulation: A Case Report

## TL;DR

A case report shows how CT scans helped diagnose a rare heart defect in a newborn, aiding surgical planning.

## Contribution

Demonstrates the diagnostic value of CT in a rare neonatal heart condition with complex anatomy.

## Key findings

- CT revealed dilated coronary arteries, right ventricle hypertrophy, and hypoplasia.
- Imaging showed a tortuous patent ductus arteriosus causing airway compression.
- CT findings influenced surgical decision-making for this complex cardiac anomaly.

## Abstract

We present a case of pulmonary atresia with intact ventricular septum and suspected right ventricle-dependent coronary circulation in a full-term neonate, highlighting the diagnostic contribution of computed tomography (CT) in evaluating a rare constellation of cardiac and airway anomalies. CT imaging demonstrated markedly dilated coronary arteries, right ventricle hypertrophy and hypoplasia, a tortuous patent ductus arteriosus causing airway compression, and complete pulmonary atresia. This complex anatomy significantly influenced the surgical decision-making process. The case illustrates CT’s role in delineating both intracardiac and extracardiac anatomy relevant to perioperative planning.