# A giant sporadic intra-abdominal desmoid tumor resection: a rare case report

## TL;DR

A 30-year-old woman with a large abdominal desmoid tumor underwent surgery, highlighting the challenges in diagnosing and treating these rare tumors.

## Contribution

This case report presents a rare, large mesenteric desmoid tumor and emphasizes the need for multidisciplinary management.

## Key findings

- The tumor required resection of the right colon and part of the ileum due to its size and location.
- The case underscores the recurrence risks and diagnostic challenges of desmoid tumors.
- Surgical planning was critical due to the tumor's proximity to major intestinal vessels.

## Abstract

Desmoid tumors (DT) are rare fibroblastic proliferations with unpredictable clinical behavior, occurring at a rate of 2 to 4 cases per million annually, predominantly in females. Prognosis is variable, with spontaneous regressions in 20 % to 30 % of cases, and shorter progression-free survival is associated with younger age, larger tumor size, and extra-abdominal location.

A 30-year-old female with chronic constipation and abdominal pain was diagnosed with a giant desmoid tumor originating from the mesentery, requiring surgical resection of the tumor, the right colon, and part of the ileum. Postoperatively, she recovered well and was referred to an oncologist for ongoing monitoring due to the tumor's potential for recurrence.

Desmoid tumors, or aggressive fibromatosis, are rare benign mesenchymal tumors characterized by local invasiveness, primarily affecting individuals aged 15 to 60, with a slight female predominance. Diagnosis is confirmed through histological evaluation and immunohistochemistry. Treatment typically involves local control through surgery and radiation, but there is a significant risk of recurrence, influenced by tumor size, location, and patient age.

This case highlights the diagnostic challenges of desmoid tumors in the mesentery, demonstrated by a 30-year-old female patient with chronic abdominal pain. The tumor, one of the largest documented, required multidisciplinary management and careful surgical planning due to its location near major intestinal vessels, emphasizing the need for prompt action and specific clinical considerations.

•A 30-year-old female with chronic abdominal pain was diagnosed with a giant mesenteric desmoid tumor.•Surgical resection was required due to its size and location.•This case underscores the diagnostic challenges and recurrence risks associated with desmoid tumors.

A 30-year-old female with chronic abdominal pain was diagnosed with a giant mesenteric desmoid tumor.

Surgical resection was required due to its size and location.

This case underscores the diagnostic challenges and recurrence risks associated with desmoid tumors.