# Dermatofibrosarcoma Protuberans of the Forehead: Case Report of a Rare Entity and Review of Literature

## TL;DR

This paper presents a rare case of forehead DFSP in a 33-year-old man who had multiple surgeries and was treated with imatinib, emphasizing the need for a multidisciplinary approach.

## Contribution

The novelty lies in reporting a rare forehead DFSP case with multiple recurrences and the use of systemic imatinib therapy.

## Key findings

- DFSP occurred in the forehead and extended to the frontal sinus in a 33-year-old male.
- The patient had three prior surgeries and was managed with systemic imatinib therapy.
- The case highlights the challenges of treating DFSP in uncommon locations.

## Abstract

Dermatofibrosarcoma protuberans (DFSP) is a rare soft tissue sarcoma originating from fibroblasts in the dermal connective tissue, comprising approximately 1% of all soft tissue sarcomas. While most cases involve the trunk and extremities, only 10%–15% occur in the cephalic region, representing less than 1% of all head and neck neoplasms. DFSP is notable for its high propensity for local recurrence following surgical excision and its low metastatic potential. We report a case of recurrent DFSP of the forehead extending to the anterior wall of the left frontal sinus, without brain involvement, in a 33-year-old male with a history of three prior wide local excisions. A multidisciplinary cancer team recommended systemic imatinib therapy. This case highlights the challenges of managing DFSP in an uncommon location, underscoring the importance of a multidisciplinary approach in addressing recurrent and complex presentations.