# Rare Case of OHVIRA with Ectopic Inguinal Hemiuterus and Ovary

## TL;DR

A 12-year-old girl was diagnosed with a rare ectopic OHVIRA syndrome, involving an inguinal ovary and hemiuterus, successfully treated with surgery.

## Contribution

This case presents a rare ectopic variant of OHVIRA syndrome with an inguinal hemiuterus and ovary, adding to the understanding of its clinical diversity.

## Key findings

- The patient had an ectopic left ovary and fallopian tube with an atretic hemiuterus in the inguinal region.
- Laparoscopy confirmed a right-sided hemiuterus and a vaginally palpable cervix, leading to a diagnosis of OHVIRA type 1.2.
- Post-surgery, the left ovary showed normal perfusion and function during 12 months of follow-up.

## Abstract

A 12-year-old girl presented with inguinal swelling and recurrent groin pain since menarche. Ultrasound showed an inguinally located ovary with normal perfusion. Herniorrhaphy revealed an ectopic inguinal left ovary with fallopian tube and atretic hemiuterus and a closed internal inguinal ring. Laparoscopy revealed a right-sided hemiuterus and vaginally palpable cervix, leading to the diagnosis of ectopic OHVIRA syndrome type 1.2. The left hemiuterus was resected and the left ovary was pulled through the inguinal canal into the abdomen. During 12 months of follow-up, the left ovary showed normal perfusion and sonomorphologic appearance, menstrual periods were uneventful.