# Right hepatectomy for primary monophasic synovial sarcoma of the liver: case report and review of the literature

## TL;DR

A rare case of liver synovial sarcoma is reported, highlighting the need for histological diagnosis and the importance of complete surgical removal for better outcomes.

## Contribution

Adds a new case of primary monophasic synovial sarcoma of the liver to the limited existing literature.

## Key findings

- Synovial sarcoma of hepatic origin is extremely rare, with only 13 cases reported.
- Complete surgical excision is the best treatment for localized liver synovial sarcoma.
- Clinical and radiological signs are not specific, requiring histological confirmation for diagnosis.

## Abstract

Synovial sarcoma is a soft-tissue sarcoma whose histological origin has long been poorly understood. It occurs mainly near the extremities of larges joints but can occur anywhere in the body. Synovial sarcoma of hepatic origin is extremely rare, with only 13 cases reported in the literature.

We report the case of a 68-year-old female patient who underwent right hepatectomy for a single 12.5 cm mass arising in the S6-S7 segments and evolving for over three years, long considered to be hepatocellular carcinoma. An Anatomopathological examination of the operative specimen showed an undifferentiated tumoral process. The immunohistochemical complement demonstrated a monophasic synovial sarcoma.

Clinical and radiological signs are not specific, and diagnosis is based on histology, of which there are three types. Complete surgical excision remains the best therapeutic option for localized forms. It may or may not be combined with adjuvant chemotherapy in other forms, although the prognosis of the disease remains guarded.

Synovial sarcoma of the liver is a rare disease with a histological diagnosis. Treatment is not standardized, and surgical excision remains the best option for localized forms.

•Primary synovial sarcoma of the liver is a rare disease. only 13 cases have been reported in the literature.•We describe the case of a 68-year-old woman whose disease occupied almost the entire right lobe with a review of the literature.•Symptoms are not specific, making histological diagnosis essential.•Emphasizes the importance of R0 excision in the traitement and prognosis of the disease.

Primary synovial sarcoma of the liver is a rare disease. only 13 cases have been reported in the literature.

We describe the case of a 68-year-old woman whose disease occupied almost the entire right lobe with a review of the literature.

Symptoms are not specific, making histological diagnosis essential.

Emphasizes the importance of R0 excision in the traitement and prognosis of the disease.