# Two-stage surgery for acute type B aortic dissection and aortic root aneurysm in a patient with Turner syndrome: a case report

## TL;DR

A 29-year-old woman with Turner syndrome underwent two-stage surgery for aortic dissection and aneurysm, achieving successful recovery.

## Contribution

This case report highlights the successful use of two-stage surgery for complex aortic conditions in a Turner syndrome patient.

## Key findings

- Two-stage surgery was effective for treating acute type B aortic dissection and aortic root aneurysm in a Turner syndrome patient.
- Postoperative echocardiography confirmed no aortic regurgitation after valve-sparing aortic root replacement.
- The patient was discharged without complications 17 days after the second surgery.

## Abstract

Patients with Turner syndrome are at high risk of aortic dissection and are more likely to present with fatal outcomes. Turner syndrome is classified as a heritable thoracic aortic disease in the latest EACTS/STS guidelines. Herein, we present a case of two-staged surgery for acute type B aortic dissection and aortic root aneurysm in a patient with Turner syndrome.

A 29-year-old female patient with Turner syndrome was admitted to our center due to back pain and was diagnosed with acute type B aortic dissection. Echocardiography revealed a dilated aortic root with bicuspid aortic valve. On the 5 th day after admission, the patient presented with a higher level of back pain. Follow-up computed tomography scan revealed changes from two- to three-channel aortic dissection a further aortic dilation. Therefore, descending aorta and partial aortic arch replacement were initially performed. Then, valve-sparing aortic root replacement and residual arch replacement were performed 3 months after the first surgery. Postoperative echocardiography confirmed the absence of aortic regurgitation. The patient was discharged on the 17th postoperative day without any complications.

Two-stage surgery was successfully performed for the thoracic aorta and aortic root aneurysms in a patient with Turner syndrome. The patient recovered for 3 months after the left thoracotomy surgery and underwent a two-stage surgery through a median sternotomy surgery with good surgical results.