# Primary Intracranial Adenoid Cystic Carcinoma: A Case Report

## TL;DR

A rare case of primary intracranial adenoid cystic carcinoma in a 61-year-old man is reported, highlighting its presentation and treatment.

## Contribution

This case report adds to the limited literature on primary intracranial adenoid cystic carcinoma, a rare and aggressive tumor.

## Key findings

- A 61-year-old male presented with neurological symptoms due to a cerebellopontine angle mass.
- Histopathological analysis confirmed the tumor as primary intracranial adenoid cystic carcinoma.
- Surgical excision was performed, but the rarity of the tumor emphasizes the need for further research.

## Abstract

Adenoid cystic carcinoma (ACC) is a rare slow-growing but aggressive malignant tumor arising from the epithelial cells of mucous-secreting glands. Primary intracranial ACC is one of the rarest entity. We report a case of a 61 years old male presenting with difficulty in swallowing, slurring of speech, generalized body weakness. Patient had residual right cerebellopontine angle (CPA) mass causing midline shift and fourth ventricular obstruction on MRI. Patient underwent right retrosigmoid craniotomy with excision of CPA mass. Histopathological examination confirmed the case as primary intracranial ACC.