# Anesthesia and Airway Management in a Child with Frank Ter Haar Syndrome Suspected Difficult Airway Undergoing Cardiac Surgery: A Case Report

## TL;DR

This case report describes anesthesia and airway management for a child with Frank ter Haar Syndrome during cardiac surgery.

## Contribution

The report highlights the challenges of managing a suspected difficult airway in a rare genetic disorder.

## Key findings

- The patient had craniofacial and skeletal abnormalities associated with a difficult airway.
- Elective surgery should be postponed until difficult airway equipment is available.

## Abstract

Frank ter Haar syndrome (FTHS) is a rare and complex multisystem congenital genetic disorder that leads to craniofacial, cardiac, and skeletal abnormalities. We report the anesthesia and airway management of a child with FTHS who was referred for repair of atrial septal defect (ASD) and ventricular septal defect (VSD).

The patient exhibited craniofacial and skeletal abnormalities, including craniosynostosis, micrognathia, a prominent forehead, hypertelorism, and anteverted nostrils. These features raised the possibility of a difficult airway.

For patients with potential difficult airways undergoing elective surgery, the procedure should be postponed until all necessary equipment for managing a difficult airway is available.