# Xanthogranulomatous pyelonephritis in a child with autoimmune joint disease

**Authors:** Pieter Willem Kriek, Maria Karsas, Jeané Cloete

PMC · DOI: 10.1007/s00467-024-06582-4 · Pediatric Nephrology (Berlin, Germany) · 2024-11-06

## TL;DR

A 7-year-old girl with juvenile arthritis was diagnosed with a rare kidney condition after a mass was found alongside a urinary tract infection.

## Contribution

This case highlights xanthogranulomatous pyelonephritis in a pediatric patient with autoimmune joint disease.

## Key findings

- Xanthogranulomatous pyelonephritis was confirmed in a 7-year-old with juvenile idiopathic arthritis.
- The condition was associated with a concurrent Escherichia coli urinary tract infection.
- Surgical excision was performed due to concerns about possible kidney cancer.

## Abstract

Xanthogranulomatous pyelonephritis is a rare condition in paediatric patients, mostly described in middle-aged female patients. We present a 7-year-old female with juvenile idiopathic arthritis, who was found to have a kidney mass with a concurrent Escherichia coli urinary tract infection. Surgical excision was done out of concern for possible malignancy. Histology confirmed the diagnosis of xanthogranulomatous pyelonephritis and persistent E. coli infection.

## Linked entities

- **Diseases:** juvenile idiopathic arthritis (MONDO:0011429), xanthogranulomatous pyelonephritis (MONDO:0007022), urinary tract infection (MONDO:0005247)

## Full-text entities

- **Diseases:** malignancy (MESH:D009369), urinary tract infection (MESH:D014552), autoimmune joint disease (MESH:D001327), kidney mass (MESH:D007674), juvenile idiopathic arthritis (MESH:D001171), Xanthogranulomatous pyelonephritis (MESH:D011705), E. coli infection (MESH:D004927)
- **Species:** Homo sapiens (human, species) [taxon 9606], Escherichia coli (E. coli, species) [taxon 562]

## Full text

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## Figures

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Source: https://tomesphere.com/paper/PMC11885348