# Successful Repair of Esophageal Atresia with Tracheoesophageal Fistula and Interrupted Inferior Vena Cava: A Rare Case Report

**Authors:** Xiao Long Mu, Junqiu Wang

PMC · DOI: 10.1055/a-2448-3530 · European Journal of Pediatric Surgery Reports · 2024-11-18

## TL;DR

A rare case of a newborn with esophageal atresia and a tracheoesophageal fistula, along with an interrupted inferior vena cava, was successfully treated with careful surgical planning.

## Contribution

Highlights a rare association of EA, TEF, and interrupted IVC, emphasizing the need for imaging to guide safe surgical repair.

## Key findings

- EA with TEF and interrupted IVC can be successfully repaired with thoracotomy.
- Prenatal and postnatal imaging is critical to identify vascular anomalies before surgery.
- Preserving the azygos vein is essential to avoid life-threatening complications.

## Abstract

Esophageal atresia (EA) with tracheoesophageal fistula (TEF) is a congenital anomaly that can present complex surgical challenges, especially when accompanied by rare vascular conditions like an interrupted inferior vena cava (IVC). The division of the azygos vein is a common part of TEF repair, but in the presence of an interrupted IVC, this can lead to life-threatening complications. We report the case of a newborn diagnosed with EA, TEF, and interrupted IVC, successfully treated through thoracotomy. This case underscores the importance of prenatal and postnatal imaging to diagnose vascular anomalies prior to TEF repair, ensuring the preservation of the azygos vein to prevent fatal outcomes. Raising awareness of this rare association is crucial to optimizing surgical planning and outcomes.

## Linked entities

- **Diseases:** esophageal atresia (MONDO:0001044), tracheoesophageal fistula (MONDO:0008586)

## Full-text entities

- **Diseases:** congenital anomaly (MESH:D000013), vascular anomalies (MESH:D020785), IVC (MESH:C563013), EA (MESH:D004933), TEF (MESH:D014138)

## Full text

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## Figures

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## References

12 references — full list in the complete paper: https://tomesphere.com/paper/PMC11869387/full.md

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Source: https://tomesphere.com/paper/PMC11869387