# A Brainstem‐Dominant Acute Disseminated Encephalomyelitis Presenting With Magnetic Resonance Imaging Findings Similar to Those of Chronic Lymphocytic Inflammation With Pontine Perivascular Enhancement Responsive to Steroid Syndrome

**Authors:** Masahiko Ezoe, Risa Hirata, Masafumi Kosugi, Masaki Tago

PMC · DOI: 10.1002/ccr3.70252 · Clinical Case Reports · 2025-02-26

## TL;DR

This paper discusses a brainstem-dominant form of acute disseminated encephalomyelitis that resembles another condition on MRI scans.

## Contribution

It highlights the importance of differentiating between two similar neurological conditions based on imaging and clinical features.

## Key findings

- Acute disseminated encephalomyelitis can present with brainstem symptoms and symmetrical basal ganglia lesions.
- Differentiation from chronic lymphocytic inflammation with pontine perivascular enhancement is crucial for proper treatment.

## Abstract

Acute disseminated encephalomyelitis can present with brainstem symptoms and bilateral symmetrical lesions in the basal ganglia. In such cases, differentiation from chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids syndrome is necessary.

## Linked entities

- **Diseases:** acute disseminated encephalomyelitis (MONDO:0019383)

## Full-text entities

- **Diseases:** Acute Disseminated Encephalomyelitis (MESH:D004673), Chronic Lymphocytic Inflammation (MESH:D015451), Steroid Syndrome (MESH:D009404)
- **Chemicals:** steroids (MESH:D013256)

## Full text

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## Figures

2 figures with captions in the complete paper: https://tomesphere.com/paper/PMC11865014/full.md

## References

3 references — full list in the complete paper: https://tomesphere.com/paper/PMC11865014/full.md

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Source: https://tomesphere.com/paper/PMC11865014