# Paediatric extra-axial myxopapillary ependymoma: what to expect? Case report and literature review

## TL;DR

This paper discusses a rare case of a low-grade brain tumor in a child, emphasizing the need for accurate diagnosis and follow-up to prevent relapse.

## Contribution

The paper presents a pediatric case of extra-axial myxopapillary ependymoma and highlights its diagnostic challenges.

## Key findings

- Extra-axial myxopapillary ependymoma is often misdiagnosed as other sacral lesions.
- Relapse with distant metastasis is common despite being a low-grade tumor.
- Proper diagnosis and follow-up are crucial for managing this condition.

## Abstract

Extra-axial ependymomas are rare tumours, and myxopapillary ependymoma (MPE) is the most common subtype in children, often misdiagnosed as other sacral lesions. MPEs are considered low-grade tumours, but relapse with distant metastasis is frequent. Therefore, therefore a proper diagnosis and subsequent follow-up are warranted. The current report presents a case of extra-axial MPE in a paediatric patient who presented with an indolent sacral mass and underwent surgical resection, along with a review of the literature. The aim was to highlight the importance of diagnostic suspicion in differential diagnosis of sacral soft-tissue masses