# Imaging findings of Budd-Chiari syndrome caused by intravenous leiomyomatosis: a case report

**Authors:** Yahong Wang, Yifan Dong, Xueyu Tian, Yu Chen, Xiao Yang, Jianchu Li

PMC · DOI: 10.3389/fmed.2024.1422652 · Frontiers in Medicine · 2024-08-13

## TL;DR

This case report describes a rare tumor causing liver vein blockage and a specific syndrome, diagnosed with imaging and successfully treated with surgery.

## Contribution

The report highlights a rare manifestation of intravenous leiomyomatosis causing Budd-Chiari syndrome, confirmed through imaging techniques.

## Key findings

- A sizable tumor obstructed the second hepatic portal, causing Budd-Chiari syndrome.
- Computed tomography venography and ultrasonography identified collateral veins and accessory hepatic vein dilation.
- Surgical resection led to a favorable prognosis for the patient.

## Abstract

Intravenous leiomyomatosis (IVL) is a rare gynecological-related tumor. It can invade and extend in the blood vessel and eventually involve the cardiac cavity or even the pulmonary artery. IVL generally does not adhere to the vein wall and infrequently leads to the manifestation of Budd-Chiari syndrome (BCS). In this case report, the presence of a sizable tumor obstructed the second hepatic portal, impeding the return flow of the hepatic veins, thereby precipitating the development of BCS. The presence of collateral veins and dilation of the accessory hepatic vein were identified through computed tomography venography and ultrasonography, thus supporting the diagnosis of BCS. The patient underwent a comprehensive surgical resection and was found to have a favorable prognosis.

## Linked entities

- **Diseases:** Budd-Chiari syndrome (MONDO:0010947), intravenous leiomyomatosis (MONDO:0003614)

## Full-text entities

- **Diseases:** tumor (MESH:D009369), IVL (MESH:D018231), gynecological-related tumor (MESH:D005833), BCS (MESH:D006502)
- **Species:** Homo sapiens (human, species) [taxon 9606]

## Full text

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## Figures

5 figures with captions in the complete paper: https://tomesphere.com/paper/PMC11347273/full.md

## References

14 references — full list in the complete paper: https://tomesphere.com/paper/PMC11347273/full.md

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Source: https://tomesphere.com/paper/PMC11347273