Biliary Atresia Associated With Jejunal Atresia: A Case Report

TL;DR

A newborn girl had two rare conditions—jejunal atresia and biliary atresia—requiring multiple surgeries and treatment.

Contribution

This case report highlights the rare co-occurrence of jejunal and biliary atresia, emphasizing diagnostic and treatment challenges.

Findings

The patient had jejunal atresia type 3a confirmed during surgery.

Post-operative MRCP indicated biliary atresia, leading to Kasai surgery.

The case underscores the need for careful management of combined gastrointestinal and biliary anomalies.

Abstract

A girl who was born at 40 weeks of gestation weighing 3800 g presented with bilious vomiting and abdominal distension shortly after birth. A lower gastrointestinal contrast study showed a microcolon with small bowel atresia. Subsequently, laparotomy, small bowel resection and anastomosis were done. Intra-operative findings noted jejunal atresia type 3a. Post-operatively, the patient developed persistent conjugated hyperbilirubinaemia and hence, magnetic resonance cholangiopancreatography (MRCP) was performed. MRCP revealed possible biliary atresia (BA) of which the patient underwent Kasai hepato-porto-enterostomy. We reported a rare case of double pathology involving jejunal atresia and BA, describing its aetiology, characteristics and treatment availability based on literature.

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