# A maxillary location of extra-nodal Rosai Dorfman disease: a case report

## TL;DR

This paper reports a rare case of Rosai-Dorfman disease in the maxillary region, highlighting its unusual presentation and successful treatment with corticotherapy.

## Contribution

The novelty lies in presenting an extra-nodal manifestation of RDD in the maxilla, expanding its known clinical spectrum.

## Key findings

- RDD was diagnosed in a 42-year-old woman with a maxillary mass confirmed via biopsy.
- Corticotherapy effectively controlled symptoms and improved the condition over one year.
- The case highlights the diagnostic challenges of extra-nodal RDD in atypical locations.

## Abstract

Introduction: Rosai-Dorfman disease (RDD) is a rare benign histiocytic proliferation, characterized by a group of clinical symptoms. This report presents a case of extranodal RDD manifesting as a progressively enlarging left maxillary mass in a 42-year-old woman. Surgical exploration and biopsy confirmed the diagnosis of RDD, with characteristic histopathological features including emperipolesis. Treatment involved corticotherapy, resulting in controlled maxillary pain and improvement of the disease after one year. This case underscores the potential for extra-nodal RDD presentations, posing diagnostic challenges and emphasizing the importance of considering RDD in the differential diagnosis of maxillary masses.