Primary Ewing’s sarcoma of the intestine: case report and literature review

TL;DR

This paper reports a rare case of Ewing's sarcoma in the intestine and highlights the difficulty in diagnosing it correctly.

Contribution

The novelty lies in presenting a case of primary Ewing's sarcoma of the intestine with a detailed clinical and pathological analysis.

Findings

CT imaging initially suggested a stromal tumor, but pathology confirmed Ewing's sarcoma.

The patient's disease progressed rapidly despite surgery and chemotherapy, leading to death.

Primary intestinal Ewing's sarcoma is rare and challenging to distinguish from other tumors.

Abstract

Ewing sarcoma (ES)/peripheral primitive neuroectodermal tumor is a highly aggressive malignant tumor that typically presents in bone and soft tissue. Primary ES of the intestine is relatively rare, which poses a challenge in distinguishing it from other primary tumors of the small intestine through imaging. This article details a case study of ES originating in the intestine. Computed tomography (CT) imaging suggested a small intestinal stromal tumor, and so the patient underwent resection of the small bowel and omental tumor. Pathology results confirmed the diagnosis of ES of the small intestine. Following surgery, the patient underwent six cycles of chemotherapy, and a follow-up positron emission tomography–CT revealed widespread dissemination of the disease with intraperitoneal metastasis, ultimately resulting in the death of the patient.

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