Right pulmonary artery originating from the ascending aorta with tetralogy of fallot and pulmonary atresia

TL;DR

This paper reports a rare heart defect where the right pulmonary artery originates from the aorta, combined with other severe conditions, requiring urgent surgical treatment.

Contribution

The paper presents a rare case combining anomalous right pulmonary artery origin with pulmonary atresia and tetralogy of Fallot.

Findings

Anomalous right pulmonary artery from the ascending aorta is a rare and life-threatening condition.

Combining this defect with pulmonary atresia and tetralogy of Fallot increases surgical complexity.

Early surgical intervention is critical for patient survival.

Abstract

Anomalous origin of right pulmonary artery from the ascending aorta is a rare congenital heart malformation that results in early infant mortality. These patients are at risk for the early development of significant pulmonary hypertension. The surgical management during the early period of life is imperative.

Anomalous pulmonary artery originating from the ascending aorta (often called hemitruncus) is a rare congenital cardiac defect requiring immediate management in the neonatal period. We report a case of a rare variant of anomalous right pulmonary artery originating from the ascending aorta in combination with pulmonary atresia and tetralogy of Fallot. The above‐mentioned combination makes the surgical management of such cardiac defect exceedingly demanding.

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