# Painless Growing Swelling on the Palm of a 4-year-old Boy: Malignant Peripheral Nerve Sheath Tumor

**Authors:** Recep Öztürk, Kemal Kösemehmetoğlu, Fisun Ardıç Yükrük, Bedii Şafak Güngör

PMC · DOI: 10.1055/s-0043-1771005 · Revista Brasileira de Ortopedia · 2023-10-24

## TL;DR

A 4-year-old boy had a painless swelling in his palm, diagnosed as a rare malignant tumor, highlighting the importance of proper diagnosis and treatment of such rare pediatric hand tumors.

## Contribution

This case report provides a clinical example of managing a rare pediatric hand tumor, emphasizing the need for accurate diagnosis in soft tissue malignancies.

## Key findings

- The patient had a slowly growing painless mass in the palm for 2 years.
- The tumor was identified as a malignant peripheral nerve sheath tumor.
- The case underscores the rarity and management challenges of pediatric hand tumors.

## Abstract

In this study, we present a 4-year-old male patient with a slowly growing painless mass in the palm of his left hand for 2 years. Although musculoskeletal tumors are rare, hand localized tumors are even rarer in pediatric patients. The fact that very few (less than one in ten) tumors are malignant and there are dozens of subtypes, each with different treatment management, shows the importance of the management of these lesions. Appropriate diagnosis and management of soft tissue masses, especially insidious malignant tumors, is vital. Due to the rarity of soft tissue tumors, adequate guidelines for their management are limited. The purpose of this report is to present an example of the approach to one of the soft tissue tumors.

Neste estudo, apresentamos um paciente do sexo masculino de 4 anos com uma massa indolor de crescimento lento na palma da mão esquerda há 2 anos. Embora os tumores musculoesqueléticos sejam raros, os tumores localizados nas mãos são ainda mais raros em pacientes pediátricos. O fato de pouquíssimos (menos de um em cada dez) tumores serem malignos e existirem dezenas de subtipos, cada um com tratamento diferente, mostra a importância do manejo dessas lesões. O diagnóstico e manejo apropriados de massas de tecidos moles, especialmente tumores malignos insidiosos, são vitais. Devido à raridade dos tumores de tecidos moles, as diretrizes adequadas para seu manejo são limitadas. O objetivo deste relato é apresentar um exemplo de abordagem de um dos tumores de partes moles.

## Linked entities

- **Diseases:** malignant peripheral nerve sheath tumor (MONDO:0004345)

## Full-text entities

- **Diseases:** soft tissue masses (MESH:D017695), mass in the (MESH:C536030), Malignant Peripheral Nerve Sheath Tumor (MESH:D018319), soft tissue tumors (MESH:D012983), hand localized tumors (MESH:D009369), Painless Growing Swelling (MESH:D004487), musculoskeletal tumors (MESH:D009140)
- **Species:** Homo sapiens (human, species) [taxon 9606]

## Full text

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## Figures

5 figures with captions in the complete paper: https://tomesphere.com/paper/PMC11254434/full.md

## References

7 references — full list in the complete paper: https://tomesphere.com/paper/PMC11254434/full.md

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Source: https://tomesphere.com/paper/PMC11254434