# Lhermitte-Duclos Disease in an Eight-Year-Old Boy: A Case Report

**Authors:** Omar M Alawaji, Ghassan M Aweja

PMC · DOI: 10.7759/cureus.62076 · Cureus · 2024-06-10

## TL;DR

This case report describes a rare brain condition called Lhermitte-Duclos disease in an eight-year-old boy and discusses possible treatment options.

## Contribution

The paper contributes a rare pediatric case report of Lhermitte-Duclos disease and highlights the need for further research on its management.

## Key findings

- Lhermitte-Duclos disease is rare in children and presents with specific clinical and radiological features.
- Surgical resection is a primary treatment option, but a conservative 'wait and see' approach is also considered.
- More studies are needed to determine optimal management strategies for LDD.

## Abstract

Lhermitte-Duclos disease (LDD), also known as dysplastic cerebellar gangliocytoma, is a rare, slow-growing, benign lesion that occurs in the cerebellum and is very uncommon in the pediatric population. There is a lack of literature and evidence about LDD management, and only one systematic review is available. Thus, more case reports and studies are warranted. This study reports a pediatric case diagnosed with LDD and describes the patient’s clinical presentation, radiological findings, and histopathological criteria. In addition, important aspects of the disease are discussed to help reach the best management options. The main management option is surgical resection, though a "wait and see" approach is also an alternative, especially for asymptomatic patients. More studies are still needed to determine the best management options.

## Linked entities

- **Diseases:** Lhermitte-Duclos disease (MONDO:0019002)

## Full-text entities

- **Diseases:** LDD (MESH:D006223)
- **Species:** Homo sapiens (human, species) [taxon 9606]

## Full text

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## Figures

3 figures with captions in the complete paper: https://tomesphere.com/paper/PMC11235393/full.md

## References

16 references — full list in the complete paper: https://tomesphere.com/paper/PMC11235393/full.md

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Source: https://tomesphere.com/paper/PMC11235393