# Retroperitoneal Sarcoma Requiring Abdominal Aortic Replacement With Long-Term Survival: A Case Report

## TL;DR

A rare case of retroperitoneal sarcoma invading the abdominal aorta was successfully treated with surgery and chemotherapy, leading to long-term survival.

## Contribution

This case report demonstrates a rare long-term survival outcome in a patient with retroperitoneal sarcoma requiring abdominal aortic replacement.

## Key findings

- The patient survived over 8 years post-surgery without recurrence.
- Combined tumor resection and abdominal aortic replacement was performed for a grade 3 retroperitoneal sarcoma.
- Postoperative chemotherapy with doxorubicin and ifosfamide was administered.

## Abstract

Retroperitoneal sarcoma (RPS) is a rare disease. RPS invading the abdominal aorta is exceedingly rare and has a poor prognosis. There have been scattered cases of RPS treated with combined abdominal aortic replacement. However, the average survival time for these cases was only 8 months, with a 2-year survival rate of 21%, indicating a poor prognosis. In this case study, a 44-year-old man presented to our hospital complaining of abdominal pain. Multiple imaging findings suggested a retroperitoneal mass that was diagnosed as a malignant tumor. The patient underwent tumor resection with abdominal aortic replacement due to an RPS tumor invading the abdominal aorta. The histopathological grade was determined to be grade 3, the most malignant grade tumor, according to the Fédération Nationale des Centres de Lutte Contre le Cancer grading system. Postoperative chemotherapy with doxorubicin and ifosfamide was administered for five cycles. The patient has been alive for over 8 years after the operation without any recurrence. This case presents a long-term survival of RPS requiring abdominal aortic replacement.