# A Rare Case of Rhabdosarcoma on the Upper Pole of the Kidney

**Authors:** Kovvuru Ashrita, Korra R Naik, Lokesh Ethuri, Sanjana Nelogal, Aisha Reshie, Sindhu C Valiveti, Mihirkumar P Parmar

PMC · DOI: 10.7759/cureus.60010 · 2024-05-09

## TL;DR

This paper reports a rare case of kidney rhabdomyosarcoma in a young child, emphasizing the need for early diagnosis and comprehensive treatment.

## Contribution

The novelty lies in documenting a rare case of rhabdomyosarcoma localized to the upper pole of the kidney in a pediatric patient.

## Key findings

- Rhabdomyosarcoma was diagnosed in a one-year-old child at the upper pole of the kidney.
- Surgical excision and histopathology confirmed the diagnosis.
- The case underscores the importance of early diagnosis and multimodal treatment for rare pediatric tumors.

## Abstract

Rhabdomyosarcoma arising from the upper pole of the kidney is an exceedingly rare occurrence, with only a few documented cases reported in the literature. Here, we present a case of a one-year-old Indian male child diagnosed with rhabdomyosarcoma localized to the upper pole of the kidney. The patient presented with abdominal distension persisting for three days, and imaging studies revealed a mass consistent with renal sarcoma. Surgical excision was performed, followed by histopathological examination confirming the diagnosis of rhabdomyosarcoma. Despite aggressive management, the patient's prognosis remains guarded due to the disease's aggressive nature. This case highlights the importance of considering rhabdomyosarcoma in the differential diagnosis of renal masses, particularly in atypical locations. Early diagnosis and a multimodal treatment approach are crucial for optimizing outcomes in such rare cases.

## Linked entities

- **Diseases:** rhabdomyosarcoma (MONDO:0005212), renal sarcoma (MONDO:0002930)
- **Species:** Homo sapiens (taxon 9606)

## Full-text entities

- **Diseases:** Rhabdomyosarcoma (MESH:D012208), renal sarcoma (MESH:D012509), renal masses (MESH:C536030), abdominal distension (MESH:D000007)
- **Species:** Homo sapiens (human, species) [taxon 9606]

## Figures

1 figure with captions in the complete paper: https://tomesphere.com/paper/PMC11162514/full.md

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Source: https://tomesphere.com/paper/PMC11162514