# Primary adrenal mantle cell lymphoma mimicking a non‐functional retroperitoneal paraganglioma

**Authors:** Kia Seyed Toutounchi, Amirreza Jabbaripour Sarmadian, Amir Vahedi, Seyed Ziaeddin Rasihashemi

PMC · DOI: 10.1002/ccr3.8887 · 2024-06-02

## TL;DR

A case of primary adrenal mantle cell lymphoma was mistaken for a non-functional retroperitoneal paraganglioma based on imaging and symptoms.

## Contribution

This case highlights the diagnostic challenge of distinguishing mantle cell lymphoma from paraganglioma using imaging alone.

## Key findings

- A retroperitoneal mass initially suspected as a paraganglioma was diagnosed as mantle cell lymphoma post-surgery.
- Histological analysis was crucial for accurate diagnosis, as imaging could not differentiate the two conditions.

## Abstract

Patients presenting with abdominal pain and retroperitoneal mass in radiographic images may be in the early stages of primary adrenal mantle cell lymphoma, which requires histological studies for a definite diagnosis.

This report presents a 37‐year‐old woman complaining of ambiguous abdominal pain, with imaging findings revealing a retroperitoneal abdominal mass on the left side of the aorta, and a possible diagnosis of non‐functional retroperitoneal paraganglioma. Total laparoscopic excision was performed. Surprisingly, histological examinations revealed features in favor of mantle cell lymphoma.

## Linked entities

- **Diseases:** mantle cell lymphoma (MONDO:0018876)

## Full-text entities

- **Diseases:** Primary adrenal mantle cell lymphoma (MESH:D020522), abdominal pain (MESH:D015746), retroperitoneal abdominal mass (MESH:C535553), retroperitoneal mass (MESH:C536030), retroperitoneal paraganglioma (MESH:D010235)
- **Species:** Homo sapiens (human, species) [taxon 9606]

## Figures

3 figures with captions in the complete paper: https://tomesphere.com/paper/PMC11144617/full.md

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Source: https://tomesphere.com/paper/PMC11144617