# A Case of Rosai-Dorfman Disease Successfully Treated by Corticotherapy

## TL;DR

A rare disease called Rosai-Dorfman disease was successfully treated with corticosteroids in an 8-year-old girl.

## Contribution

This case report highlights the successful use of corticosteroids in treating Rosai-Dorfman disease in a pediatric patient.

## Key findings

- The patient showed a favorable outcome after treatment with oral corticosteroids.
- There was no recurrence after one year of follow-up.

## Abstract

Rosai-Dorfman disease (RDD) is a benign histiocytic proliferation that results in nodal and extranodal involvements. It is a rare disease, with fewer than 1,000 cases reported in the literature, which explains its lack of knowledge by physicians and the lack of codified therapeutic strategies. We report the case of an 8-year-old girl who presented a rapidly progressive cervical lymph node mass; the diagnosis of RDD was made based on histology and immunohistochemistry. The patient was treated with oral corticosteroids at a dose of 1 mg/kg/d with a favorable outcome and no recurrence after one year of follow-up. This observation illustrates the clinical presentation and diagnosis of this rare clinicopathological entity. The prognosis and treatment options are also discussed.