# A Rare Case of Adult Cervicothoracic Cystic Lymphangioma Presenting as Neurogenic Thoracic Outlet Syndrome

**Authors:** Majed A Almourgi

PMC · DOI: 10.7759/cureus.56146 · Cureus · 2024-03-14

## TL;DR

A rare case of a cystic lymphangioma in an adult caused neurogenic thoracic outlet syndrome and was successfully treated with surgery.

## Contribution

This case report highlights the rare presentation of adult-onset cervicothoracic cystic lymphangioma causing neurogenic thoracic outlet syndrome and its effective surgical management.

## Key findings

- A 38-year-old male presented with a cervicothoracic cystic lymphangioma causing neurogenic thoracic outlet syndrome.
- Complete surgical excision via a left supraclavicular approach successfully removed the cyst with no recurrence after 19 months.
- A multimodal diagnostic approach is essential to differentiate cystic lymphangioma from other neck masses.

## Abstract

Cystic lymphangioma (CL) is an uncommon congenital malformation of the lymphatic system, often occurring in the head, neck, or mediastinum, potentially causing compression symptoms like dysphagia or dyspnea, and in rare cases, neurogenic thoracic outlet syndrome (nTOS). This report details a case of a 38-year-old male with a four-year history of a left lower neck mass, experiencing tingling in his left forearm over the last six months. The examination revealed a left supraclavicular cystic mass, with imaging suggesting CL compressing neurovascular structures. The patient underwent successful complete surgical excision through a left supraclavicular approach. Histopathology confirmed CL, with no recurrence observed over 19 months. The case highlights that cervicothoracic CL with adult presentation can cause pressure symptoms including nTOS. It also underscores the role of a multimodal diagnostic approach to differentiate it from other neck masses and that a supraclavicular approach can effectively remove the cyst, especially when the lower extension is not deep and there is no surrounding inflammation, thereby leading to relieving pressure and preventing recurrence.

## Linked entities

- **Diseases:** cystic lymphangioma (MONDO:0009761), neurogenic thoracic outlet syndrome (MONDO:0015061)

## Full-text entities

- **Diseases:** dyspnea (MESH:D004417), tingling (MESH:D010292), Adult Cervicothoracic Cystic Lymphangioma (MESH:D018191), dysphagia (MESH:D003680), neck mass (MESH:D006258), congenital malformation of the lymphatic system (MESH:C567452), inflammation (MESH:D007249), cyst (MESH:D003560), compression (MESH:D009408), Neurogenic Thoracic Outlet Syndrome (MESH:D013901)
- **Species:** Homo sapiens (human, species) [taxon 9606]

## Full text

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## Figures

5 figures with captions in the complete paper: https://tomesphere.com/paper/PMC11015715/full.md

## References

15 references — full list in the complete paper: https://tomesphere.com/paper/PMC11015715/full.md

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Source: https://tomesphere.com/paper/PMC11015715