# Unveiling Dermatomyositis: A Tragic Tale of Mortality in a 23-Year-Old

**Authors:** Vinit Deolikar, Sarang S Raut, Saket Toshniwal, Shilpa A Gaidhane, Sourya Acharya

PMC · DOI: 10.7759/cureus.56058 · 2024-03-12

## TL;DR

This paper presents a case of a young woman who died from dermatomyositis, a rare muscle disease, without any signs of cancer.

## Contribution

The novelty lies in documenting a rare, fatal case of dermatomyositis in a young adult without malignancy.

## Key findings

- A 23-year-old female died from dermatomyositis complications.
- No malignancy was detected in the patient.
- Diagnosis relied on clinical and laboratory findings.

## Abstract

Dermatomyositis represents a rare inflammatory myopathy that induces inflammation in the muscles or related tissues, including the blood vessels supplying these muscles. The precise pathogenesis of this condition remains unknown. Diagnosis typically relies on clinical indicators such as skin rashes, progressive muscle weakness, elevated serum muscle enzymes, abnormal electromyogram results, and muscle biopsy. In this case study, we report a fatal case of dermatomyositis in a 23-year-old female patient who succumbed to complications of dermatomyositis, causing mortality without any evidence of malignancy.

## Linked entities

- **Diseases:** dermatomyositis (MONDO:0016367)

## Full-text entities

- **Diseases:** inflammatory myopathy (MESH:D009220), Mortality (MESH:D003643), muscle weakness (MESH:D018908), malignancy (MESH:D009369), skin rashes (MESH:D005076), Dermatomyositis (MESH:D003882), inflammation (MESH:D007249)
- **Species:** Homo sapiens (human, species) [taxon 9606]

## Figures

6 figures with captions in the complete paper: https://tomesphere.com/paper/PMC11009825/full.md

---
Source: https://tomesphere.com/paper/PMC11009825