Dural Arteriovenous Fistula in Neuro-Behçet's Disease: Association or Chance?

TL;DR

This paper presents a case of a 48-year-old man with neuro-Behçet's disease and a dural arteriovenous fistula, exploring whether the two are related or a coincidence.

Contribution

The novelty lies in presenting a case and reviewing literature to investigate the potential association between dAVF and Behçet's disease.

Findings

A case of NBD with dAVF was successfully treated with prednisolone, colchicine, and surgical resection.

The paper discusses the possible but debated link between BD and dAVF based on recent literature.

The case adds to the limited evidence on the co-occurrence of BD and dAVF.

Abstract

Behçet's disease (BD) is a multisystemic vasculitis disorder. Neuro-Behçet's disease (NBD) is a set of neurologic symptoms imputable to an underlying Behçet vasculitis. Among the wide range of vascular abnormalities secondary to BD, a dural arteriovenous fistula (dAVF) is not classically described. Whether a dAVF is associated with BD or dAVF is a chance occurrence is still a matter of debate. Herein, we describe an NBD case of a 48-year-old male, presenting with headache and fever, where a dAVF was seen on imaging. He was treated with prednisolone and colchicine, followed by the surgical resection for dAVF. Then, we discuss the possible association between BD and dAVF based on the latest literature.

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