# High-Grade Atypical Teratoid/Rhabdoid Tumor in the Pituitary Region

## TL;DR

A rare case of a brain tumor called AT/RT was found in the pituitary region of a 37-year-old woman, highlighting the challenges of treating such tumors in adults.

## Contribution

This case report adds to the limited literature on AT/RT in adults by describing a rare presentation and treatment approach.

## Key findings

- An AT/RT was diagnosed in the pituitary region of a 37-year-old female.
- The patient underwent surgery followed by chemotherapy and radiation.
- The patient passed away 14 months later from unrelated causes.

## Abstract

Atypical teratoid/rhabdoid tumors (AT/RTs) are embryological tumors of the central nervous system (CNS). They are typically found in children, with rare presentations in adults. We describe the presentation of an AT/RT in the pituitary region of a 37-year-old female. The patient presented with a two-week history of intractable cephalgia with sudden onset of monocular diplopia and left-sided cranial nerve VI palsy. The patient underwent transsphenoidal resection of their mass, which revealed the diagnosis. She then underwent systemic therapy with chemotherapy as well as radiation. She ultimately died 14 months after treatment completion due to unrelated events. The case highlights the rarity of AT/RT in adults, emphasizing the challenge of establishing standardized treatment protocols due to its rarity in adult presentations.