# Left Main Stem Compression by Intrapericardial Paraganglioma Associated With Succinate Dehydrogenase Mutation

## TL;DR

A rare heart tumor caused by a genetic mutation was found to compress a major coronary artery in a young woman.

## Contribution

This case report highlights a novel association between a succinate dehydrogenase A mutation and an intrapericardial paraganglioma.

## Key findings

- A primary cardiac paraganglioma was identified encasing the left main stem coronary artery.
- The tumor was linked to a succinate dehydrogenase A gene mutation.
- The patient presented with dyspnea and subscapular pain due to left main stem compression.

## Abstract

Paragangliomas are rare extra-adrenal tumors originating from chromaffin cells. We discovered a large intrapericardial mass confirmed to be a primary cardiac paraganglioma encasing the left main stem coronary artery in a 38-year-old woman who presented with dyspnea and subscapular pain. Genetic predisposition related to succinate dehydrogenase A mutation was identified.