# Atypical Clinical Presentation of Xanthogranulomatous Pyelonephritis in a Female Child: A Case Report

**Authors:** Kamel A Alenazi

PMC · DOI: 10.7759/cureus.53666 · 2024-02-05

## TL;DR

This case report describes a rare kidney disease in a healthy child, showing atypical symptoms and a good prognosis after treatment.

## Contribution

The paper presents an unusual case of XGPN in a child, highlighting its atypical clinical presentation.

## Key findings

- XGPN was diagnosed in a child with flank pain, an uncommon presentation.
- The patient was otherwise healthy, which is atypical for this condition.
- Nephrectomy was performed, and the prognosis was favorable.

## Abstract

Xanthogranulomatous pyelonephritis (XGPN) is an uncommon chronic obstructive renal suppuration disease. Histopathologically, XGPN manifests as lipid-laden macrophage infiltration in renal microstructure and inflammation of an engorged non-functional kidney. Nephrectomy is the standard therapeutic treatment, and the overall prognosis is good. Here, we report a case of XGPN presented as flank pain in an otherwise healthy child.

## Linked entities

- **Diseases:** Xanthogranulomatous pyelonephritis (MONDO:0007022)

## Full-text entities

- **Diseases:** XGPN (MESH:D011705), chronic obstructive renal suppuration disease (MESH:D051436), inflammation (MESH:D007249), flank pain (MESH:D021501)

## Figures

1 figure with captions in the complete paper: https://tomesphere.com/paper/PMC10918298/full.md

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Source: https://tomesphere.com/paper/PMC10918298