# Paediatric dermatofibrosarcoma protuberan—a case report in an Afro-Caribbean boy

## TL;DR

A 9-year-old Afro-Caribbean boy was diagnosed with a rare skin tumor called dermatofibrosarcoma protuberans, which is uncommon in children and has a good outlook.

## Contribution

This is the first reported case of pediatric dermatofibrosarcoma protuberans in the Caribbean region and the institution.

## Key findings

- The tumor was successfully biopsied with a 2-mm margin and later excised with a 4-cm margin.
- After 6 months of follow-up, there has been no recurrence of the tumor.
- Long-term surveillance for recurrence is planned for at least 5 years.

## Abstract

Dermatofibrosarcoma protuberans is a rare low-grade sarcoma, which rarely metastasizes, but it is locally aggressive with a propensity to recur. It usually affects persons of African descent and is extremely rare in childhood with a favourable prognosis. We present a case of paediatric dermatofibrosarcoma protuberans to the midline of the lower back of a 9-year-old Afro-Caribbean boy who was biopsied with a 2-mm margin. After histological confirmation, a 4-cm margin was then performed. Surveillance for recurrence, though none has been seen thus far after 6-month follow-up, will be done for at least 5 years and possibly longer, given this is the first case of this nature ever seen in our institution and the Caribbean region.